Table 1

Clinical features of primary pleural angiosarcomas (epithelioid haemangioendothelioma)

Case Sex Age (years) Clinical Radiology Course (months) Necroscopic findings
1M59Pleuritic pain, dyspnoeaEffusion, diffuse pleural thickening, plaques (CXR, CT)7Diffuse pleural tumour, hyaline pleural plaques, ferruginous bodies in lung
2M73Chest infection, dyspnoeaEffusion, pleural fibrosis,pleural mass, plaque (CXR,CT)9Diffuse pleural tumour, pleural fibrosis, classical asbestos bodies in lung
3M33Cough, pleuritic pain, dyspnoeaEffusion, parietal pleural thickening, diaphragm and pericardial spread (CXR, CT)8Diffuse pleural neoplasm with local invasion of mediastinum and diaphragm. Contralateral plaque. Ferruginous bodies, many coarse “welding type”